产品名称:
OTC
产品货号:
PLD-500
别名 :
OCTD
实验类型 :
IHC-P
反应种属 :
Human
宿主物种 :
Rabbit
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背景
This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. [provided by RefSeq, Jul 2008]
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细胞定位
线粒体基质
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基因 ID
5009
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Swiss Prot
P00480
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别名
OCTD
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反应种属
Human
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实验类型
IHC-P
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推荐稀释比
1:100
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宿主物种
Rabbit
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克隆性
Monoclonal
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同位型
IgG
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纯化方式
Affinity Purification
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偶联物
Un-conjugated
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储存条件
Store at -20°C. Supplied in 50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% sodium azide and 0.05% BSA. Stable for 12 months from date of receipt.